Share with Facebook Share with Twitter Share with Linkedin Send by email Enlarge the text Reduce the text Our apps QUESTION D'ACTU [/H3]
World Charcot's Disease Day: the majority of patients disappear in three to five years - By Margot Montpezat
On this World Charcot's Day, we explain why the majority of patients disappear in three to five years. [/H4]
Lars Neumann-
-
-
-
-
-
- Published on 21.06.2022 at 11:00
| -
| -
| -
| -
- Key words :
- charcot disease
- world Day
- sick
THE ESSENTIAL
Today is World Amyotrophic Lateral Sclerosis (ALS) Day.
It is estimated that in France there are between 7,000 and 8,000 people suffering from ALS.
The name “Charcot” comes from the French neurologist who first described amyotrophic lateral sclerosis (ALS). In English, it is also called Lou Gehrig's disease, in homage to a famous baseball player affected by this disease….
Whatever the name given to this degenerative disorder, the reality for patients suffering from this disease which leads to progressive paralysis with a fatal outcome is the same: since there is currently no treatment, they watch helplessly as their body.
ALS takes different forms depending on the nature of the initial damage, as indicated by Inserm: “In about 30% of cases, it begins in the brainstem. We then speak of forms with bulbar onset, the first manifestations of which are difficulties in articulating or swallowing. In the other cases, ALS first alters the peripheral motor neurons: in these forms with spinal onset, it is through weakness and discomfort in an arm, a leg or a hand that manifests itself. the beginning of the disease”.
[H3] Neurons [/H3]
ALS affects the neurons (nerve cells) and prevents the transmission of information between the brain and the muscles of the whole body, which gradually causes the disease to intensify and reach all the muscles up to the respiratory muscles which precipitates its worsening. Concretely, there is muscle wasting, coordination disorders that prevent walking and picking up objects. Difficulties swallowing or articulating increase. The brain remains unscathed.
Its causes are unknown: in one out of ten cases a genetic cause is suspected, but the onset of the disease probably depends on various factors, environmental and genetic. It generally appears between the ages of 50 and 70, and often earlier when it is of family origin. The outcome is fatal after 3 to 5 years of evolution on average and most often, it is the attack of the respiratory muscles which causes the death of the patients.
[H3] “Only your eyes and your brain work” [/H3]
On Europe 1, Christophe Malsot, 57, commercial director who discovered that he had the disease 18 months ago, explains: "You start not being able to breathe on your own, you lose your speech, and only your your eyes and your brain work. Today, when the diagnosis is made, you are told that you are going to die. 80% of people disappear between three and five years of age." According to him, "this is the reason why many people [affected] decide to say: 'It's over, I prefer to leave.'" For him, the choice is already made: "if at some point, that became too vegetative, that's what I would like to do." The case of the famous astrophysicist Stephen Hawking diagnosed at the dawn of his 21 years and died in 2018 at the age of 76 having lived fifty years with this disease remains a mystery.
[H3] Therapeutic tracks [/H3]
No curative treatment is yet available but the medium-term prospects are encouraging with several therapeutic avenues under study with the search for relevant biological markers.
Their identification could facilitate the early diagnosis of the disease in families with affected persons: "it is in fact established that neurodegenerative diseases cause biological and morphological changes several years before the appearance of the first symptoms. However, this stage pre-symptomatic probably represents the best window for therapeutic intervention to prevent the neurodegenerative process, before it causes irreversible damage” according to Inserm.
ON THE SAME THEME [/H3]
Sleep: how can the way we sleep cause the onset of Charcot's disease?
Charcot's disease: a blood test to easily detect it
Intense sport can trigger Charcot's disease
Like this article ? Sign up to the newsletter ! Register WE RECOMMEND [/H2]
Resumption of the Covid-19 pandemic: we will have to "live with the disease" [/H3]
How diet does or does not stimulate prostate cancer [/H3]
Monkey pox: the High Authority of Sante specifies the vaccination strategy [/H3]
One in eight people live with a mental disorder according to WHO [/H3]
WE RECOMMEND [/H3]
Resumption of the Covid-19 pandemic: we will have to "live with the disease"
How diet does or does not stimulate prostate cancer
Monkey pox: the High Authority for Health specifies the vaccination strategy
One in eight people live with a mental disorder according to the WHO Send to a friend [/H4]
Your Name: Your Email: Your friend's email: Your friend's name: Leave your message: What is 4 + 1? : Close Send
LIVE [/H2]
Resumption of the Covid-19 pandemic: we will have to "live with the disease"
How diet does or does not stimulate prostate cancer
Monkey pox: the High Authority for Health specifies the vaccination strategy
Charcot's disease: the majority of patients disappear in three to five years
One in eight people live with a mental disorder, according to WHO
Why are women more stressed on Wednesdays?
A compound in red wine would help to age in good health
How to tell if eggs are still good
A plant-based diet lowers the risk of breast cancer
Actress Charlotte Valandrey gets another heart transplant
Iron deficiency: how to remedy it sustainably through food
Hygiene: what is the best frequency to take a shower?
Here's why you should never reuse a plastic bottle after the water is finished
6 signs of poor health visible on your eyes
Flatulence: these food sources to avoid to overcome gas
Blueberries: this precious red fruit that we should eat more
Gout attack: sugary drinks are not recommended
Why favor physical activity to treat depression?
A hernia operation, a little boy undergoes a vasectomy
Why pollen allergies are more severe this year
Diet: what diet when you quit smoking?
Mosquitoes have an Achilles heel in their genes
Grand Est: three departments colonized by this dangerous mosquito
"Drugs and alcohol": Bradley Cooper confides in his addictions THE HEALTH CHANNEL [/H2]
[H4] Multiple sclerosis: how to cope? [/H4]
Multiple sclerosis is an inflammatory disease of the central nervous system. It now affects 100,000 people...
[H4] My life with multiple sclerosis [/H4]
Multiple sclerosis is an inflammatory disease of the central nervous system. It now affects 100,000 people...
[H4] Electronic cigarette: friend or foe? [/H4]
It is an object that is now part of our daily lives but which is not without danger to health. While the High Council...
[H4] Lung cancer: screening could change everything [/H4]
It is responsible for the highest number of cancer deaths in France. Yet better screening for lung cancer...
[H4] My life with schizophrenia [/H4]
Schizophrenia is a psychiatric illness characterized by a set of highly variable symptoms: the most ...
[H4] My life with HIV [/H4]
AIDS or Acquired Immune Deficiency Syndrome is the ultimate stage of infection by the human immunodeficiency virus...
[H4] What are the treatments for osteoporosis? [/H4]
Each year, osteoporosis is responsible for nearly 400,000 fractures in France. Beyond its effect on the skeleton in ...
[H4] What is osteoporosis? [/H4]
Each year, osteoporosis is responsible for nearly 400,000 fractures in France. Why Doctor takes stock.
[H4] The simple method to treat anxiety and depression [/H4]
Dr. David Gourion, psychiatrist in Paris, comes to present his new book to us. It's a quick and easy way to...
[H4] My life with polycystic ovary syndrome (PCOS) [/H4]
Polycystic ovary syndrome (PCOS) is the most common hormonal disease in women of childbearing age.
DISEASES [/H2]
Hematoma and bruise: the importance or the circumstances require medical advice [/H3]
Sunburn: a skin burn that puts you at risk of cancer [/H3]
Heatstroke, sunstroke: hyperthermia that should never be overlooked [/H3]
I HAVE HURT [/H3]
SYMPTOMS [/H2]
Period disorders: a frequent hormonal imbalance [/H3]
Stomach ache in adults: behind the banal abdominal pain, the fear of urgency [/H3]
Resumption of the Covid-19 pandemic: we will have to "live with the disease"
How diet does or does not stimulate prostate cancer
Monkey pox: the High Authority for Health specifies the vaccination strategy
One in eight people live with a mental disorder, according to WHO
The reference health site with daily all the medical news deciphered by practicing doctors and the advice of the best specialists. ABOUT [/H3]
- Personal data and cookies
- Who are we
- Conditions of use
